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ESID Grand Rounds 14: Contemporary Management of DN-STAT3 / Job’s syndrome

Date: Tuesday, 14 March 2023, 17:00 CET Topic: Contemporary Management of DN-STAT3 / Job’s syndrome. Panel: Alexandra Freeman, MD Bodo Grimbacher, MD, PhD Johannes Rädler, MD, Resident Andrew Gennery, MD, PhD Moderator: Fabian Hauck, MD, PhD Description: AD-HIES / Job’s syndrome is a multisystem disorder with hematopoietic and extra-hematopoietic manifestations. Conservative treatment is based on skin and mucosal care, anti-infective drugs, immunoglobulin replacements, and more recently biologicals targeting allergic inflammation. Still, significant morbidity and mortality affect quality of live and overall survival of patients with DN-STAT3 and their families. Allogeneic hematopoietic cell transplantation (HCT) at present is not routinely recommended because initial attempts have documented poor outcome. More recently, however, paralleling major improvements in HCT and supportive care, individual centers are beginning to offer HCT to select patients. This webinar on contemporary management of DN-STAT3 / Job’s syndrome aims at providing most recent information on conservative treatment and HCT to facilitate patient counseling and treatment decision making. After participating in this webinar, participants should be able to: . Discuss clinical manifestations of DN-STAT3 / Job’s syndrome . Describe conservative treatment of DN-STAT3 / Job’s syndrome . Assess allogeneic hematopoietic cell transplantation for DN-STAT3 / Job’s syndrome